![]() ![]() patients are less symptomatic or may even be asymptomatic.spina bifida may be present, but other vertebral anomalies are far less common.cord divided, sometimes incompletely so.Type II is milder than type I, and lack many of the features of the latter: patients are usually symptomatic presenting with scoliosis and tethered cord syndrome.skin pigmentation, hemangioma, and hypertrichosis (hair patch) are common.vertebral abnormalities: hemivertebrae, butterfly vertebrae, spina bifida, fusion of laminae of adjacent levels.midline spur often present (osseous or osteocartilaginous).Type I is the classic diastematomyelia, characterized by 1-6: type II: single dural sac containing both hemicords impairment less marked.type I: duplicated dural sac, with common midline spur (osseous or fibrous) and usually symptomatic.Split cord malformations are divided into two types according to the presence of a dividing septum and single vs dual dural sac: Specifically, it has been thought that a persistent or abnormal adhesion between the ectoderm and endoderm creates an additional neuroenteric canal which in turn leads to the notocord developing into two hemicords 8. The condition is believed to occur during the gastrulation stage of development due to abnormal movement and separation of precursor cells 7. ![]() Patients with diastematomyelia also frequently have other associated anomalies including: The majority of patients with diastematomyelia are symptomatic, presenting with signs and symptoms of tethered cord, although patients with mild type II (see below) may be minimally affected or entirely asymptomatic 6. Split cord malformations are a congenital abnormality and account for ~5% of all congenital spinal defects 6. For the purposes of this article, the terms diastematomyelia and split cord malformation are used interchangeably. Although traditionally it has been distinguished from diplomyelia (in which the cord is duplicated rather than split) the term split cord malformation is advocated to encompass both conditions 6. ![]()
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